A 10-day-old infant presented with hematuria. Multiple CT images show a large heterogeneous mass originating from the lower pole of the right kidney (cortical beak sign noted, pink arrow). The mass extends into the right renal pelvis and causes mild hydronephrosis.
- Synonyms: mesoblastic nephroma, leiomyomatous hamartoma, mesenchymal hamartoma, renal fibroma, Bolande tumor.
- It is the most common solid renal tumor in the newborn.
- This tumor is believed to arise from metanephric blastema or secondary mesenchyme.
- Patients usually presents with a palpable flank mass.
- Prognosis is excellent with nephrectomy and wide resection
- Large solid intrarenal mass, which typically involves or extends to the renal sinus.
- Hemorrhage, necrosis or cystic portions are uncommon.
Table: Age Presentation of Renal Tumors in Children
1. Donnelly LF. Diagnostic imaging pediatrics. Amirsys. Manitoba. 2005.
2. Lowe LH, Isuani BH, Heller RM, Stein SM, Johnson JE, Navarro OM, Hernanz-Schulman M. Pediatric renal masses: Wilms tumor and beyond. Pediatric renal masses: Wilms tumor and beyond. Radiographics. 2000; 20:1585-603.